Poly-GR Increased Ferroptosis Vulnerability in C9orf72-ALS Cells

Poly-GR Increased Ferroptosis Vulnerability in C9orf72-ALS Cells

TL;DR: A 2026 study in Cell & Bioscience found that poly-GR, a toxic repeat protein linked to C9orf72-ALS, pushed motor neuron-like cells toward ferroptosis by raising lipid peroxidation and ferrous iron while weakening the Nrf2/Slc7a11 antioxidant pathway. Key Findings GR50 model: Researchers expressed EGFP-GR50, a 50-repeat glycine-arginine poly-GR construct, in NSC-34 motor neuron-like cells. Ferroptosis …

Read more

TDP43 Failure Disrupts DNA Repair in ALS and FTD

The Broken Repair Crew: How TDP43 Sabotages Genome Stability TL;DR: TDP43, the protein that misfires in ALS and FTD, secretly controls DNA repair genes—and when it breaks, mutations pile up in neurons, potentially explaining both neurodegeneration and the cancer link in these diseases. A protein known for its role in neurodegenerative disease has a hidden …

Read more